Neurol. praxi. 2013;14(2):105-108
Neuromyotonia
- 1 Neurologická klinika FN Ostrava
- 2 Oddělení imunologie a alergologie, Zdravotní ústav se sídlem v Ostravě
We have described case of the young man with a rare diagnosis of acquired neuromyotonia with neuromuscular signs and symptoms of
autonomic dysfunction. Except specific electromyographic findings, the diagnosis is documented by positive antibodies against voltage-
-gated slow potassium channels. Due the assumption of paraneoplastic etiology the patient underwent comprehensive examination
with no evidence of malignancy. The patient was treated with immunosuppressive, immunomodulatory therapy and symptomatic medications.
Remission was achieved within several months and it is a question wether it was treatment effect or spontaneous remission.
Keywords: neuromyotonia, Isaacs syndrom, myokymia, anti VGKC
Published: April 1, 2013 Show citation
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